Diffuse retinal involvement in malignant nonteratoid medulloepithelioma of ciliary body in an adult.

Intraocular medulloepithelioma is a rare embryonal neoplasm that occurs predominantly in children and arises from the primitive medullary epithelium of the optic cup. Medulloepitheliomas that contain heterotopic elements or tissues such as brain, cartilage, or rhabdomyoblasts are classified as teratoid, and tumors lacking these elements are classified as nonteratoid medulloepitheliomas. Both nonteratoid and teratoid medulloepitheliomas may be benign or malignant. The clinical and histopathological features of intraocular medulloepitheliomas have been described previously in various reports. We herein report a case of a malignant nonteratoid medulloepithelioma of a ciliary body in an adult. To the best of our knowledge, this is the first documented report of a medulloepithelioma of the ciliary body with intraretinal involvement.